Adamantinoma_ A Rare Bone Tumor Overview

Adamantinoma (from Greek adamantinos 'very hard') is a rare bone cancer, making up less than 1% of all bone cancers."
"The slow-growing tumor predominantly arises in long bones in a subcortical location (95% in the tibia or fibula)."
"Benign osteofibrous dysplasia may be a precursor of adamantinoma or a regressive phase of adamantinoma."
"X-rays of the affected area show a well defined tumour in bone, with multiple lobules giving a 'soap bubble' appearance."
"Treatment consists of wide resection or amputation."
"Metastases are rare at presentation but may occur in up to 30% of patients during the disease course. Prognosis is excellent, with overall survival of 85% at 10 years, but is lower when wide surgical margins cannot be obtained."